Chronic Granulomatous Disease in a Boy Who Presented With Dactilitis Caused by Serratia Marcescens, Mimicking Rheumatic Monoarthritis in the Newborn Period: A Case Presentation
1Division of Immunology, Department of Pediatrics, Erciyes University Faculty of Medicine, Kayseri, Turkey
2Department of Pediatrics, Erciyes University Faculty of Medicine, Kayseri, Turkey
3Department of Immunology, Erciyes University Faculty of Medicine, Kayseri, Turkey
J Clin Pract Res 2018; 40(2): 95-98 DOI: 10.5152/etd.2018.0102
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Abstract

Chronic granulomatous disease (CGD) is a heterogenous genetic primary immune deficiency disorder, characterized by lifethreatening infections and granulomas secondary to increased inflammatory responses. Most infections involve the lungs, skin, lymph nodes, and liver. Wedescribe a child diagnosed with CGD and the p67phox mutation presenting with Serratia marcescens arthritis without osteomyelitis in the newborn period.