Case Report
Congenital Lobar Emphysema
1Clinic of Pediatrics, Kayseri Training and Research Hospital, Kayseri, Turkey
2Clinic of Pediatric Allergy, Kayseri Training and Research Hospital, Kayseri, Turkey
3Clinic of Radiology, Kayseri Training and Research Hospital, Kayseri, Turkey
4Division of Pediatric Chest Diseases, Erciyes University Faculty of Medicine, Kayseri, Turkey
5Clinic of Pediatric Hemotology, Kayseri Training and Research Medicine, Kayseri, Turkey
2Clinic of Pediatric Allergy, Kayseri Training and Research Hospital, Kayseri, Turkey
3Clinic of Radiology, Kayseri Training and Research Hospital, Kayseri, Turkey
4Division of Pediatric Chest Diseases, Erciyes University Faculty of Medicine, Kayseri, Turkey
5Clinic of Pediatric Hemotology, Kayseri Training and Research Medicine, Kayseri, Turkey
J Clin Pract Res 2015; 37(3): 122-124 DOI: 10.5152/etd.2015.8528
Abstract
Congenital lobar emphysema is a rare developmental abnormality characterized by overinflation of one or more of the pulmonary lobes. This disease presents as respiratory distress because of the ventilation perfusion mismatch as a result of the hyperinflated lung causing compression atelectasis on the ipsilateral or contralateral side with mediastinal shift. Surgical resection of the affected lobes is indicated in both, unless symptoms resolve with conservative therapy. Here, we present a 40-day-old female child requiring right middle lobectomy who presented with respiratory distress caused by congenital lobar emphysema.
Keywords: Congenital lobar emphysema, respiratory distress, lobectomy