Background: Mature cystic teratomas are the most common germ cell tumors of the ovary. Both malign and benign tumors may arise inside the mature teratomas. Only 42 cases of pulmonary papillary adenomas are described in the literature with only 2 cases of pulmonary papillary adenoma inside a mature cystic teratoma of ovary.
Case report: This case report highlights the presence of a pulmonary papillary adenoma in a mature cystic teratoma of the ovary in a 28-year-old woman, which is the third case of literature This case report also includes review of the literature discussing its histomorphological and immunohistochemical features.
Conclusion: Pulmonary papillary adenomas within ovarian mature cystic teratomas represents an exceedingly rare phenomenon warranting further research .