Staged Surgical Treatment in an Infant with Huge Aortopulmonary Window Presenting with Severe Pulmonary Hypertension and Recurrent Pulmonary Infection

Özyurt, Abdullah; Tunçay, Aydın; Tekerek, Nazan U.; Akyıldız, Başak N.; Koç, Gonca; Doğanay, Selim; Narin, Nazmi

doi:10.5152/etd.2015.140002

Case Report

Staged Surgical Treatment in an Infant with Huge Aortopulmonary Window Presenting with Severe Pulmonary Hypertension and Recurrent Pulmonary Infection

Abdullah Özyurt ¹ , Aydın Tunçay ² , Nazan U. Tekerek ³ , Başak N. Akyıldız ³ , Gonca Koç ⁴ , Selim Doğanay ⁴ , Nazmi Narin ¹

¹Division of Pediatric Cardiology, Erciyes University Faculty of Medicine, Kayseri, Turkey
²Department of Pediatric Cardiovascular Surgery, Erciyes University Faculty of Medicine, Kayseri, Turkey
³Department of Pediatric Intensive Care, Erciyes University Faculty of Medicine, Kayseri, Turkey
⁴Department of Pediatric Radiology, Erciyes University Faculty of Medicine, Kayseri, Turkey

J Clin Pract Res 2015; 37(4): 157-161 DOI: 10.5152/etd.2015.140002

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Abstract

Aortopulmonary window (APW) is a very rare congenital aortic septation defect in which early diagnosis followed by an immediate repair is crucial. Severe pulmonary hypertension may develop even in early infancy as it occurred in our current case. Herein, we report a 4-month-old male who underwent staged surgical closure of a large APW presenting with severe pulmonary hypertension and recurrent pulmonary infection.

Keywords: Congenital Abnormalities, Aortopulmonary Window, Pneumonia, Pulmonary Hypertension, surgical closure